American Journal of Internal Medicine

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Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis

Received: Jun. 27, 2018    Accepted: Jul. 23, 2018    Published: Aug. 24, 2018
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Abstract

Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.

DOI 10.11648/j.ajim.20180605.12
Published in American Journal of Internal Medicine ( Volume 6, Issue 5, September 2018 )
Page(s) 94-98
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Alveolar Microlithiasis, Rheumatoid Arthritis, Sputum Positive Pulmonary Tuberculosis

References
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[6] Al-Sardar H, Al-Habbo DJ, Al-Hayali RM Pulmonary alveolar microlithiasis: report of two brothers with the same illness and review of literature. BMJ Case Rep. 2014 Mar 31; 2014. pii: bcr2013201300. doi: 10.1136/bcr-2013-201300. Review. PMID: 24686795.
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Cite This Article
  • APA Style

    Arti Sharma, Abhay Uppe, Shahid Patel, Girija Nair. (2018). Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. American Journal of Internal Medicine, 6(5), 94-98. https://doi.org/10.11648/j.ajim.20180605.12

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    ACS Style

    Arti Sharma; Abhay Uppe; Shahid Patel; Girija Nair. Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. Am. J. Intern. Med. 2018, 6(5), 94-98. doi: 10.11648/j.ajim.20180605.12

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    AMA Style

    Arti Sharma, Abhay Uppe, Shahid Patel, Girija Nair. Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. Am J Intern Med. 2018;6(5):94-98. doi: 10.11648/j.ajim.20180605.12

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  • @article{10.11648/j.ajim.20180605.12,
      author = {Arti Sharma and Abhay Uppe and Shahid Patel and Girija Nair},
      title = {Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis},
      journal = {American Journal of Internal Medicine},
      volume = {6},
      number = {5},
      pages = {94-98},
      doi = {10.11648/j.ajim.20180605.12},
      url = {https://doi.org/10.11648/j.ajim.20180605.12},
      eprint = {https://download.sciencepg.com/pdf/10.11648.j.ajim.20180605.12},
      abstract = {Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.},
     year = {2018}
    }
    

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    T1  - Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis
    AU  - Arti Sharma
    AU  - Abhay Uppe
    AU  - Shahid Patel
    AU  - Girija Nair
    Y1  - 2018/08/24
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    N1  - https://doi.org/10.11648/j.ajim.20180605.12
    DO  - 10.11648/j.ajim.20180605.12
    T2  - American Journal of Internal Medicine
    JF  - American Journal of Internal Medicine
    JO  - American Journal of Internal Medicine
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    EP  - 98
    PB  - Science Publishing Group
    SN  - 2330-4324
    UR  - https://doi.org/10.11648/j.ajim.20180605.12
    AB  - Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.
    VL  - 6
    IS  - 5
    ER  - 

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Author Information
  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Section